Caroli's Disease (CD) is as a rare congenital condition characterized by non-obstructive saccular or fusiform dilatation of the intra-hepatic bile ducts of the liver.
Caroli’s disease is an extremely rare disorder; 1 case per 1,000,000 populations. It is inherited with autosomal recessive pattern.
Incidence of Caroli's disease is equal in men and women and the disease usually manifests either in neonates or in the early adulthood.
| Figure 1: Dilation of the intrahepatic bile ducts|